protein
Adenylate kinase isoenzyme 1
aka AK 1
Gene
AK1
Organism
Homo sapiens(9606)
Length
194 aa
Mass
21,635 Da
Adenylate kinase isoenzyme 1 (AK1) is a 194-amino acid phosphotransferase that catalyzes reversible transfer of the terminal phosphate group between ATP and AMP, playing a central role in cellular energy homeostasis and adenine nucleotide metabolism (UniProt: P00568). The enzyme also displays broad nucleoside diphosphate kinase activity and can catalyze thiamine triphosphate synthesis at very low rates. AK1 is associated with congenital non-spherocytic hemolytic anemia (CNSHA3, MIM 612631), an autosomal recessive condition characterized by hemolytic anemia and erythrocyte adenylate kinase deficiency (UniProt: P00568).
AK1 is relevant to Alzheimer's Disease pathology. In human post-mortem AD brain tissue compared to age-matched controls, AK1 protein levels are elevated (mean log2FC = 1.0949) in subcellular fractions analyzed by TMT-labeled mass spectrometry (Chaparral AD proteomics). This upregulation may reflect compensatory responses to energy metabolism disruption or changes in subcellular compartmentalization characteristic of AD neurodegeneration.
Generated from the curated entity record below. May contain errors — verify against source links.
Proteomics Evidence · AD
↑ Up in ADP3
+1.095
P2
not detected
S2
not detected
S3
not detected
Mean log₂FC across detected fractions: +1.0949 (1 of 4 fractions detected)
Human post-mortem AD brain vs age-matched controls, TMT-labeled, 4 subcellular fractions (P2, P3, S2, S3), DDA proteomics.
Related Publications
Browse all →Tau molecular diversity contributes to clinical heterogeneity in Alzheimer's disease.
Dujardin Simon et al.Nature medicine2020PMID 32572268Deep Multilayer Brain Proteomics Identifies Molecular Networks in Alzheimer's Disease Progression.
Bai Bing et al.Neuron2020PMID 31926610A Multi-network Approach Identifies Protein-Specific Co-expression in Asymptomatic and Symptomatic Alzheimer's Disease.
Seyfried Nicholas T et al.Cell systems2017PMID 27989508Large-scale deep multi-layer analysis of Alzheimer's disease brain reveals strong proteomic disease-related changes not observed at the RNA level.
Johnson Erik C B et al.Nature neuroscience2022PMID 35115731Organization and regulation of gene transcription.
Cramer PatrickNature2019PMID 31462772
Function
Catalyzes the reversible transfer of the terminal phosphate group between ATP and AMP. Also displays broad nucleoside diphosphate kinase activity. Plays an important role in cellular energy homeostasis and in adenine nucleotide metabolism (By similarity) (PubMed:21080915, PubMed:23416111, PubMed:2542324). Also catalyzes at a very low rate the synthesis of thiamine triphosphate (ThTP) from thiamine diphosphate (ThDP) and ADP (By similarity)
Disease associations
Anemia, congenital, non-spherocytic hemolytic, 3CNSHA3
An autosomal recessive disease characterized by hemolytic anemia and undetectable erythrocyte adenylate kinase activity.
Sources
Last updated 5/8/2026, 6:35:31 AM
